Types
- Limited cutaneous (CREST) — skin involvement of hands, face; calcinosis, Raynaud's, esophageal dysmotility, sclerodactyly, telangiectasias
- Diffuse cutaneous — extensive skin involvement, more lung/kidney/heart risk
Treatment
- Raynaud's: calcium channel blockers, lifestyle
- Skin: emollients, immunosuppressants
- Lung disease: immunosuppressants, antifibrotics
- Renal crisis: ACE inhibitors (essential)
- GI: acid suppression, prokinetics
- Pulmonary hypertension treatment
Medical Disclaimer: This information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always consult a qualified healthcare provider with questions about a medical condition. If you are experiencing a medical emergency, call your local emergency number immediately.
References
- ACR. Systemic Sclerosis Information.