Behçet's Disease
Behçet's disease is a rare chronic inflammatory disorder causing blood vessel inflammation throughout the body. Hallmarks include recurrent mouth ulcers, genital ulcers, eye inflammation, and skin lesions.
Quick Facts
- ICD-10: M35.2
- Common in: Middle East, East Asia
Symptoms
- Recurrent painful mouth ulcers (almost universal)
- Genital ulcers
- Eye inflammation (uveitis) — can threaten vision
- Skin lesions (acne-like, erythema nodosum)
- Joint pain
- Vascular inflammation (vein clots, aneurysms)
- Neurologic involvement (rare but serious)
- GI involvement
Diagnosis
Clinical — based on recurrent oral ulcers plus other features. There is no specific lab test. Pathergy test (skin pinprick) is sometimes positive.
Treatment
- Topical corticosteroids for mouth/genital ulcers
- Colchicine for mucocutaneous symptoms
- Systemic corticosteroids for severe involvement
- Immunosuppressants (azathioprine, cyclosporine)
- Biologics (anti-TNF, apremilast)
Medical Disclaimer: This information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always consult a qualified healthcare provider with questions about a medical condition. If you are experiencing a medical emergency, call your local emergency number immediately.
References
- American Behçet's Disease Association. Patient Resources.